Cholangiocarcinoma in choledochal cyst after cystoenterostomy: how a mistreated choledochal cyst can progress to malignancy
نویسندگان
چکیده
This case report presents an unusual case of cholangiocarcinoma arising nearly 35 years after cystoduodenostomy for choledochal cyst. The patient visited our hospital with dyspepsia and studies revealed bezoar within the choledochal cyst caused by bile and food reflux. The patient underwent pancreaticoduodenectomy and a biopsy revealed adenocarcinoma, stage IIB. After 19 months, the patient has no recurrence to date and has recovered well. This case shows that proper surgical management and meticulous, long-term follow-up is imperative for patients with congenital choledochal cyst.
منابع مشابه
Metachronous cholangiocarcinoma 13 years post resection of choledochal cyst—is long-term follow-up useful?: a case study and review of the literature
BACKGROUND Patients with congenital choledochal cyst are at risk of the development of hepatobiliary malignancy, with recommended treatment of choledochal cyst being surgical excision. The development of cholangiocarcinoma more than 10 years after excision of choledochal cysts is rare, with less than 21 cases reported in the literature from 1972 to 2014. This is the first reported case of metac...
متن کاملMetastatic Cholangiocarcinoma following Choledochal Cyst Excision: An Unusual Cause of Abdominal Pain in a 35-Year-Old Female
Choledochal cysts are anomalous arrangements of the pancreaticobiliary tract and a well-known aetiology for cholangiocarcinoma. The risk of cholangiocarcinoma in patients with an unresected choledochal cyst remains at 20-30%1. Of the five types of choledochal cyst, by far the most common is the extrahepatic fusiform (Type I). Management involves complete excision of the extrahepatic bile duct a...
متن کاملA rare case of non-metastatic cholangiocarcinoma in a long standing choledochal cyst
Choledochal cysts are rare benign growths that can develop into cancerous lesions if left untreated. The cysts are commonly discovered incidentally during imaging procedures for other reasons. Surgical resection is recommended to avoid risk of cancer or metastatic disease. A rare case of a non-metastatic cholangiocarcinoma in a longstanding choledochal cyst is presented in this case report.
متن کاملOccurrence of signet-ring cell carcinoma with cholangiocarcinoma 25 years after choledochal cyst excision
RATIONALE Choledochal cysts are a risk factor for the development of cholangiocarcinoma. Hence, complete surgical excision is the preferred treatment in most cases. However, cholangiocarcinoma still can develop from the remnant biliary system after surgical excision. Signet-ring cell carcinoma is a rare type of cancer of the biliary system, and the occurrence of signet-ring cell carcinoma after...
متن کامل[A case of intrahepatic cholangiocarcinoma associated with Type IV choledochal cyst].
Anomalous union of the pancreaticobiliary duct (AUPBD) is a congenital anomaly that is defined as a junction of the bile duct and pancreatic duct outside the duodenal wall. This anomaly results in a loss of normal sphincteric mechanisms at the pancreaticobiliary junction. As a result, regurgitation of pancreatic juice into the biliary system develops and causes choledochal cysts, choledocholith...
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عنوان ژورنال:
دوره 20 شماره
صفحات -
تاریخ انتشار 2016